Description
Antibody Name: | RHAG Antibody |
Antibody SKU: | PACO01985 |
Size: | 50ug |
Host Species: | Rabbit |
Tested Applications: | ELISA, WB |
Recommended Dilutions: | WB:1:500-1:2000 |
Species Reactivity: | Human |
Immunogen: | synthesized peptide derived from the N-terminal region of human CD241. |
Form: | Liquid |
Storage Buffer: | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
Purification Method: | The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen. |
Clonality: | Polyclonal |
Isotype: | IgG |
Conjugate: | Non-conjugated |
Synonyms: | RHAG; RH50; Ammonium transporter Rh type A; Erythrocyte membrane glycoprotein Rh50; Erythrocyte plasma membrane 50 kDa glycoprotein; Rh50A; Rhesus blood group family type A glycoprotein; |
UniProt Protein Function: | RHAG: Associated with rhesus blood group antigen expression. May be part of an oligomeric complex which is likely to have a transport or channel function in the erythrocyte membrane. Defects in RHAG are the cause of regulator type Rh-null hemolytic anemia (RHN); also known as Rh-deficiency syndrome. RHN is a form of chronic hemolytic anemia in which the red blood cells have a stomatocytosis and spherocytosis morphology, an increased osmotic fragility, an altered ion transport system, and abnormal membrane phospholipid organization. Belongs to the ammonium transporter (TC 2.A.49) family. Rh subfamily.Protein type: Membrane protein, integral; Membrane protein, multi-pass; Transporter; Transporter, SLC familyChromosomal Location of Human Ortholog: 6p12.3Cellular Component: integral to plasma membrane; membrane; plasma membraneMolecular Function: ammonium transmembrane transporter activity; ankyrin binding; leak channel activityBiological Process: ammonium transport; bicarbonate transport; carbon dioxide transport; cellular ion homeostasis; monovalent inorganic cation transport; nitrogen utilization; organic cation transportDisease: Overhydrated Hereditary Stomatocytosis; Rh-null, Regulator Type |
UniProt Protein Details: | |
NCBI Summary: | The protein encoded by this gene is erythrocyte-specific and is thought to be part of a membrane channel that transports ammonium and carbon dioxide across the blood cell membrane. The encoded protein appears to interact with Rh blood group antigens and Rh30 polypeptides. Defects in this gene are a cause of regulator type Rh-null hemolytic anemia (RHN), or Rh-deficiency syndrome.[provided by RefSeq, Mar 2009] |
UniProt Code: | Q02094 |
NCBI GenInfo Identifier: | 731174174 |
NCBI Gene ID: | 6005 |
NCBI Accession: | BAP94457.1 |
UniProt Secondary Accession: | Q02094,O43514, O43515, Q7L8L3, Q9H454, B2R8T8 |
UniProt Related Accession: | Q02094 |
Molecular Weight: | 38,420 Da |
NCBI Full Name: | Rh-associated glycoprotein |
NCBI Synonym Full Names: | Rh-associated glycoprotein |
NCBI Official Symbol: | RHAG |
NCBI Official Synonym Symbols: | OHS; RH2; OHST; Rh50; CD241; RH50A; Rh50GP; SLC42A1 |
NCBI Protein Information: | ammonium transporter Rh type A |
UniProt Protein Name: | Ammonium transporter Rh type A |
UniProt Synonym Protein Names: | Erythrocyte membrane glycoprotein Rh50; Erythrocyte plasma membrane 50 kDa glycoprotein; Rh50A; Rhesus blood group family type A glycoprotein; Rh family type A glycoprotein; Rh type A glycoprotein; Rhesus blood group-associated ammonia channel; Rhesus blood group-associated glycoprotein; CD_antigen: CD241 |
Protein Family: | Ammonium transporter |
UniProt Gene Name: | RHAG |
UniProt Entry Name: |