Description
Antibody Name: | PEX1 Antibody (PACO54038) |
Antibody SKU: | PACO54038 |
Size: | 50ug |
Host Species: | Rabbit |
Tested Applications: | ELISA, IHC, IF |
Recommended Dilutions: | ELISA:1:2000-1:10000, IHC:1:20-1:200, IF:1:50-1:200 |
Species Reactivity: | Human |
Immunogen: | Recombinant Human Peroxisome biogenesis factor 1 protein (927-1283AA) |
Form: | Liquid |
Storage Buffer: | Preservative: 0.03% Proclin 300 Constituents: 50% Glycerol, 0.01M PBS, pH 7.4 |
Purification Method: | >95%, Protein G purified |
Clonality: | Polyclonal |
Isotype: | IgG |
Conjugate: | Non-conjugated |
Immunohistochemistry analysis of human placenta tissue using PACO54038 at dilution of 1:100. | |
Immunofluorescent analysis of HepG2 cells using PACO54038 at dilution of 1:100 and Alexa Fluor 488-congugated AffiniPure Goat Anti-Rabbit IgG(H+L). |
Background: | Required for stability of PEX5 and protein import into the peroxisome matrix. Anchored by PEX26 to peroxisome membranes, possibly to form heteromeric AAA ATPase complexes required for the import of proteins into peroxisomes. |
Synonyms: | Peroxisome biogenesis factor 1 (Peroxin-1) (Peroxisome biogenesis disorder protein 1), PEX1 |
NCBI Summary: | This gene encodes a member of the AAA ATPase family, a large group of ATPases associated with diverse cellular activities. This protein is cytoplasmic but is often anchored to a peroxisomal membrane where it forms a heteromeric complex and plays a role in the import of proteins into peroxisomes and peroxisome biogenesis. Mutations in this gene have been associated with complementation group 1 peroxisomal disorders such as neonatal adrenoleukodystrophy, infantile Refsum disease, and Zellweger syndrome. Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Sep 2013] |
UniProt Code: | O43933 |
NCBI GenInfo Identifier: | 4505725 |
NCBI Gene ID: | 5189 |
NCBI Accession: | NP_000457.1 |
UniProt Related Accession: | O43933 |
Molecular Weight: | |
NCBI Full Name: | peroxisome biogenesis factor 1 isoform 1 |
NCBI Synonym Full Names: | peroxisomal biogenesis factor 1 |
NCBI Official Symbol: | PEX1 |
NCBI Official Synonym Symbols: | ZWS; ZWS1; HMLR1; PBD1A; PBD1B |
NCBI Protein Information: | peroxisome biogenesis factor 1 |
UniProt Protein Name: | Peroxisome biogenesis factor 1 |
UniProt Synonym Protein Names: | Peroxin-1; Peroxisome biogenesis disorder protein 1 |
Protein Family: | Peroxisomal ATPase |
UniProt Gene Name: | PEX1 |
UniProt Entry Name: | PEX1_HUMAN |