Description
Antibody Name: | PEX1 Antibody |
Antibody SKU: | PACO04577 |
Size: | 50ug |
Host Species: | Rabbit |
Tested Applications: | ELISA, IHC |
Recommended Dilutions: | IHC:1:100-1:300 |
Species Reactivity: | Human, Mouse |
Immunogen: | synthesized peptide derived from the C-terminal region of human Peroxin 1. |
Form: | Liquid |
Storage Buffer: | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
Purification Method: | The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen. |
Clonality: | Polyclonal |
Isotype: | IgG |
Conjugate: | Non-conjugated |
Synonyms: | PEX1; Peroxisome biogenesis factor 1; Peroxin-1; Peroxisome biogenesis disorder protein 1 |
NCBI Summary: | This gene encodes a member of the AAA ATPase family, a large group of ATPases associated with diverse cellular activities. This protein is cytoplasmic but is often anchored to a peroxisomal membrane where it forms a heteromeric complex and plays a role in the import of proteins into peroxisomes and peroxisome biogenesis. Mutations in this gene have been associated with complementation group 1 peroxisomal disorders such as neonatal adrenoleukodystrophy, infantile Refsum disease, and Zellweger syndrome. Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Sep 2013] |
UniProt Code: | O43933 |
NCBI GenInfo Identifier: | 4505725 |
NCBI Gene ID: | 5189 |
NCBI Accession: | NP_000457.1 |
UniProt Related Accession: | O43933 |
Molecular Weight: | |
NCBI Full Name: | peroxisome biogenesis factor 1 isoform 1 |
NCBI Synonym Full Names: | peroxisomal biogenesis factor 1 |
NCBI Official Symbol: | PEX1 |
NCBI Official Synonym Symbols: | ZWS; ZWS1; HMLR1; PBD1A; PBD1B |
NCBI Protein Information: | peroxisome biogenesis factor 1 |
UniProt Protein Name: | Peroxisome biogenesis factor 1 |
UniProt Synonym Protein Names: | Peroxin-1; Peroxisome biogenesis disorder protein 1 |
Protein Family: | Peroxisomal ATPase |
UniProt Gene Name: | PEX1 |
UniProt Entry Name: | PEX1_HUMAN |