Human MCEE Recombinant Protein (RPES4594)

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SKU:
RPES4594
Product Type:
Recombinant Protein
Species:
Human

Description

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Human MCEE Recombinant Protein

Methylmalonyl-CoA epimerase, mitochondrialµmCEE?is an enzyme which belongs to the glyoxalase I family. It converts (S)-methylmalonyl-CoA to the (R) form, catalyses the following chemical reaction: (R)-methylmalonyl-CoA (S)-methylmalonyl-CoA. It plays an important role in the catabolism of fatty acids with odd-length carbon chains. This protein deficiency is an autosomal recessive inborn error of AA metabolism, involving valine, threonine, isoleucine and methionine. This organic aciduria can appear in the neonatal period with life-threatening metabolic acidosis, hyperammonemia, feeding difficulties, pancytopenia and coma.

Product Name:Human MCEE Recombinant Protein (RPES4594)
Product Code:RPES4594
Size:10µg
Species:Human
Expressed Host:Human Cells
Synonyms:Methylmalonyl-CoA epimerase, mitochondrial,DL-methylmalonyl-CoA racemase
Accession:Q96PE7
Sequence:Gln37-Ala176
Fusion tag:C-6His
Endotoxin:<1.0 EU per µg as determined by the LAL method.
Protein Construction:Recombinant Human Methylmalonyl-CoA epimerase is produced by our Mammalian expression system and the target gene encoding Gln37-Ala176 is expressed with a 6His tag at the C-terminus.
Purity:> 95 % as determined by reducing SDS-PAGE.
Mol Mass:16.0 kDa
AP Mol Mass:18-20 kDa
Formulation:Supplied as a 0.2 µm filtered solution of 20mM TrisHCl,150mM NaCl,1mM DTT,10%Glycerol,pH7.5.
Shipping:This product is provided as liquid. It is shipped at frozen temperature with blue ice/gel packs.Upon receipt, store it immediately at<-20°C.
Stability and Storage:Store at < -20°C, stable for 6 months. Please minimize freeze-thaw cycles.
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