Metabolism Recombinant Proteins

Human FBPase 1/FBP1 Recombinant Protein (RPES3740)

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SKU:
RPES3740
Product Type:
Recombinant Protein
Species:
Human
Research Area:
Metabolism

Description

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Human FBPase 1/FBP1 Recombinant Protein

Fructose-1;6-Bisphosphatase 1 (FBPase 1) is a member of the FBPase class 1 family. FBPase 1 is a gluconeogenesis regulatory protein; which catalyzes the hydrolysis of fructose 1;6-bisphosphate to fructose 6-phosphate and inorganic phosphate. FBPase 1 can assume an active R-state; or an inactive T-state. FBPase 1 deficiency is inherited as an autosomal recessive disorder mainly in the liver and causes life-threatening episodes of hypoglycemia and metabolic acidosis in newborn infants or young children. FBPase 1 coupled with phosphofructokinase (PFK) is involved in the metabolism of pancreatic islet cells.

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