Description
Antibody Name: | CRYBB3 Antibody (PACO08617) |
Antibody SKU: | PACO08617 |
Size: | 50ul |
Host Species: | Rabbit |
Tested Applications: | ELISA, WB, IF |
Recommended Dilutions: | |
Species Reactivity: | Human, Mouse, Rat |
Immunogen: | Human CRYBB3 |
Form: | Liquid |
Storage Buffer: | PBS with 0.02% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles. |
Purification Method: | Antigen Affinity purified |
Clonality: | Polyclonal |
Isotype: | IgG |
Conjugate: | Non-conjugated |
Synonyms: | crystallin, β B3;CRYBB3;CATCN2;CRYB3;MGC125772;MGC125773;MGC125774 ;Beta-B3 crystallin; Beta-crystallin B3 |
UniProt Protein Function: | CRYBB3: a major structural protein of the eye lens. A member of the beta/gamma-crystallin family. Protein type: CytoskeletalChromosomal Location of Human Ortholog: 22q11.23Molecular Function: protein bindingDisease: Cataract 22, Multiple Types |
UniProt Protein Details: | |
NCBI Summary: | Crystallins are separated into two classes: taxon-specific, or enzyme, and ubiquitous. The latter class constitutes the major proteins of vertebrate eye lens and maintains the transparency and refractive index of the lens. Since lens central fiber cells lose their nuclei during development, these crystallins are made and then retained throughout life, making them extremely stable proteins. Mammalian lens crystallins are divided into alpha, beta, and gamma families; beta and gamma crystallins are also considered as a superfamily. Alpha and beta families are further divided into acidic and basic groups. Seven protein regions exist in crystallins: four homologous motifs, a connecting peptide, and N- and C-terminal extensions. Beta-crystallins, the most heterogeneous, differ by the presence of the C-terminal extension (present in the basic group, none in the acidic group). Beta-crystallins form aggregates of different sizes and are able to self-associate to form dimers or to form heterodimers with other beta-crystallins. This gene, a beta basic group member, is part of a gene cluster with beta-A4, beta-B1, and beta-B2. Mutations in this gene result in cataract congenital nuclear autosomal recessive type 2. [provided by RefSeq, Feb 2013] |
UniProt Code: | P26998 |
NCBI GenInfo Identifier: | 311033476 |
NCBI Gene ID: | 1417 |
NCBI Accession: | P26998.4 |
UniProt Secondary Accession: | P26998,Q3B7S9, Q3T1B7, Q6ISK6, Q92965, Q9UH09 |
UniProt Related Accession: | P26998 |
Molecular Weight: | 24,252 Da |
NCBI Full Name: | Beta-crystallin B3 |
NCBI Synonym Full Names: | crystallin beta B3 |
NCBI Official Symbol: | CRYBB3 |
NCBI Official Synonym Symbols: | CRYB3; CATCN2; CTRCT22 |
NCBI Protein Information: | beta-crystallin B3 |
UniProt Protein Name: | Beta-crystallin B3 |
UniProt Synonym Protein Names: | Beta-B3 crystallin |
Protein Family: | Beta-crystallin |
UniProt Gene Name: | CRYBB3 |
UniProt Entry Name: | CRBB3_HUMAN |