Description
Antibody Name: | ALMS1 Antibody (PACO62563) |
Antibody SKU: | PACO62563 |
Size: | 50ul |
Host Species: | Rabbit |
Tested Applications: | ELISA, IF |
Recommended Dilutions: | ELISA:1:2000-1:10000, IF:1:50-1:200 |
Species Reactivity: | Human |
Immunogen: | Recombinant Human Alstrom syndrome protein 1 protein (889-1057AA) |
Form: | Liquid |
Storage Buffer: | Preservative: 0.03% Proclin 300 Constituents: 50% Glycerol, 0.01M PBS, pH 7.4 |
Purification Method: | >95%, Protein G purified |
Clonality: | Polyclonal |
Isotype: | IgG |
Conjugate: | Non-conjugated |
Immunofluorescence staining of Hela cells with PACO62563 at 1:133, counter-stained with DAPI. The cells were fixed in 4% formaldehyde, permeabilized using 0.2% Triton X-100 and blocked in 10% normal Goat Serum. The cells were then incubated with the antibody overnight at 4°C. The secondary antibody was Alexa Fluor 488-congugated AffiniPure Goat Anti-Rabbit IgG(H+L). |
Background: | Involved in PCM1-dependent intracellular transport. Required, directly or indirectly, for the localization of NCAPD2 to the proximal ends of centrioles. Required for proper formation and/or maintenance of primary cilia (PC), microtubule-based structures that protrude from the surface of epithelial cells. |
Synonyms: | Alstrom syndrome protein 1, ALMS1, KIAA0328 |
UniProt Protein Function: | Involved in PCM1-dependent intracellular transport. Required, directly or indirectly, for the localization of NCAPD2 to the proximal ends of centrioles. Required for proper formation and/or maintenance of primary cilia (PC), microtubule-based structures that protrude from the surface of epithelial cells. |
UniProt Protein Details: | |
NCBI Summary: | This gene encodes a protein containing a large tandem-repeat domain as well as additional low complexity regions. The encoded protein functions in microtubule organization, particularly in the formation and maintanance of cilia. Mutations in this gene cause Alstrom syndrome. There is a pseudogene for this gene located adjacent in the same region of chromosome 2. Alternative splice variants have been described but their full length nature has not been determined. [provided by RefSeq, Apr 2014] |
UniProt Code: | Q8TCU4 |
NCBI GenInfo Identifier: | 110349786 |
NCBI Gene ID: | 7840 |
NCBI Accession: | NP_055935.4 |
UniProt Secondary Accession: | Q8TCU4,Q53S05, Q580Q8, Q86VP9, Q9Y4G4, A0A087WZY3 |
UniProt Related Accession: | Q8TCU4 |
Molecular Weight: | |
NCBI Full Name: | Alstrom syndrome protein 1 |
NCBI Synonym Full Names: | ALMS1 centrosome and basal body associated protein |
NCBI Official Symbol: | ALMS1 |
NCBI Official Synonym Symbols: | ALSS |
NCBI Protein Information: | Alstrom syndrome protein 1 |
UniProt Protein Name: | Alstrom syndrome protein 1 |
UniProt Synonym Protein Names: | |
Protein Family: | Alstrom syndrome protein |
UniProt Gene Name: | ALMS1 |
UniProt Entry Name: |
Antibodies |
ALMS1 Antibody (PACO00388) |
Secondary Antibody |
Anti-HRP Goat Anti-Rabbit IgG (H+L) Antibody (CABS014) |
Recommended Products |
Anti-FITC Goat Anti-Rabbit IgG (H+L) Antibody (CABS011) |
Anti-HRP-conjugated Beta Actin Antibody (CABC028) |