Name: ACAD8 Antibody (PACO15248)
SKU: PACO15248
Availability: OutOfStock

Form:	Liquid
Storage Buffer:	-20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
Purification Method:	Antigen affinity purification
Clonality:	Polyclonal
Isotype:	IgG
Conjugate:	Non-conjugated

	The image on the left is immunohistochemistry of paraffin-embedded Human thyroid cancer tissue using PACO15248(ACAD8 Antibody) at dilution 1/15, on the right is treated with fusion protein. (Original magnification: x200).
	The image on the left is immunohistochemistry of paraffin-embedded Human colon cancer tissue using PACO15248(ACAD8 Antibody) at dilution 1/15, on the right is treated with fusion protein. (Original magnification: x200).

Background:	This gene encodes a member of the acyl-CoA dehydrogenase family of enzymes that catalyze the dehydrogenation of acyl-CoA derivatives in the metabolism of fatty acid, or branch chained amino acid, The encoded protein is a mitochondrial enzyme that functions in catabolism of the branched-chain amino acid, valine. Defects in this gene are the cause of isobutyryl-CoA dehydrogenase deficiency.
Synonyms:	acyl-CoA dehydrogenase family, member 8

UniProt Protein Function:
UniProt Protein Details:
NCBI Summary:	This gene encodes a member of the acyl-CoA dehydrogenase family of enzymes that catalyze the dehydrogenation of acyl-CoA derivatives in the metabolism of fatty acids or branch chained amino acids. The encoded protein is a mitochondrial enzyme that functions in catabolism of the branched-chain amino acid valine. Defects in this gene are the cause of isobutyryl-CoA dehydrogenase deficiency.[provided by RefSeq, Nov 2009]
UniProt Code:	Q9UKU7
NCBI GenInfo Identifier:	26006699
NCBI Gene ID:	27034
NCBI Accession:	Q9UKU7.1
UniProt Secondary Accession:	Q9UKU7
UniProt Related Accession:	Q9UKU7
Molecular Weight:	39kDa
NCBI Full Name:	Isobutyryl-CoA dehydrogenase, mitochondrial
NCBI Synonym Full Names:	acyl-CoA dehydrogenase family member 8
NCBI Official Symbol:	ACAD8
NCBI Official Synonym Symbols:	ARC42; ACAD-8
NCBI Protein Information:	isobutyryl-CoA dehydrogenase, mitochondrial
UniProt Protein Name:
UniProt Synonym Protein Names:
Protein Family:	Isobutyryl-CoA dehydrogenase
UniProt Gene Name:
UniProt Entry Name: